Treatment for hemophilia depends on
the type and the severity of the disorder.
Patients can actually
replace their clotting factor.
This can be done for a factors VIII and IX, and
this product comes from donated human blood
and you can also have a recombinant
clotting factor and this is made in a lab.
The good news is patients
can actually self infuse at home.
Another medication option is desmopressin which is
DDAVP and this can help stimulate factor VIII release.
A patient with hemophilia A can live a relatively
normal life when their condition is managed well
and they receive appropriate check-ups at a
comprehensive hemophilia treatment center.
But even with good hemophilia
care, complications can develop
and when they do, they usually
require immediate medical attention
since these complications
can be life threatening.
One is deep internal bleeding.
This is bleeding that can occur in the deep
muscle and can cause the limbs to swell.
The swelling compress on the
nerves and lead to numbness or pain.
The patient can also develop
hematuria or blood in the urine.
They may develop life-threatening
hemorrhages and this includes into the brain.
And remember the bleeding into
the joints, this is gonna cause damage.
It's gonna cause pain and arthritis
and eventual destruction of the joint.
This can also press on the nerves.
Another complication is severe
anemia due to the massive blood loss.
This can cause it's own
cascade of complications including
putting extra strain on the heart,
kidney and respiratory systems.
Infection is next.
Patients with hemophilia are more
likely to have blood transfusions
increasing the risk of receiving
contaminated blood products.
You can also have an adverse
reaction to the clotting factor treatment.
In some patients with hemophilia, the
immune system has a negative reaction
to these clotting factors
used to treat their bleeding.
When this happens, the immune system
develops proteins known as inhibitors
that inactivate the clotting factors
making the treatment less effective.