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Hemophilia: Management and Complications (Pediatric Nursing)

by Paula Ruedebusch

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    00:00 Treatment for hemophilia depends on the type and the severity of the disorder.

    00:05 Patients can actually replace their clotting factor.

    00:08 This can be done for a factors VIII and IX, and this product comes from donated human blood and you can also have a recombinant clotting factor and this is made in a lab.

    00:17 The good news is patients can actually self infuse at home.

    00:22 Another medication option is desmopressin which is DDAVP and this can help stimulate factor VIII release.

    00:30 A patient with hemophilia A can live a relatively normal life when their condition is managed well and they receive appropriate check-ups at a comprehensive hemophilia treatment center.

    00:39 But even with good hemophilia care, complications can develop and when they do, they usually require immediate medical attention since these complications can be life threatening.

    00:49 One is deep internal bleeding.

    00:51 This is bleeding that can occur in the deep muscle and can cause the limbs to swell.

    00:55 The swelling compress on the nerves and lead to numbness or pain.

    00:59 The patient can also develop hematuria or blood in the urine.

    01:03 They may develop life-threatening hemorrhages and this includes into the brain.

    01:07 And remember the bleeding into the joints, this is gonna cause damage.

    01:10 It's gonna cause pain and arthritis and eventual destruction of the joint.

    01:14 This can also press on the nerves.

    01:17 Another complication is severe anemia due to the massive blood loss.

    01:21 This can cause it's own cascade of complications including putting extra strain on the heart, kidney and respiratory systems.

    01:29 Infection is next.

    01:30 Patients with hemophilia are more likely to have blood transfusions increasing the risk of receiving contaminated blood products.

    01:37 You can also have an adverse reaction to the clotting factor treatment.

    01:41 In some patients with hemophilia, the immune system has a negative reaction to these clotting factors used to treat their bleeding.

    01:48 When this happens, the immune system develops proteins known as inhibitors that inactivate the clotting factors making the treatment less effective.


    About the Lecture

    The lecture Hemophilia: Management and Complications (Pediatric Nursing) by Paula Ruedebusch is from the course Blood Disorders – Pediatric Nursing.


    Included Quiz Questions

    1. Replacement of clotting factor XII or IX
    2. Packed red blood cell infusions
    3. Bone marrow transplant
    4. Iron supplements

    Author of lecture Hemophilia: Management and Complications (Pediatric Nursing)

     Paula Ruedebusch

    Paula Ruedebusch


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