So in a nutshell, hemophilia is a rare
disorder in which the blood doesn't clot normally
because it lacks sufficient blood clotting
proteins - these are the clotting factors.
Hemophilia A has a defect with Factor VIII
and hemophilia B has a defect with factor IX.
There are acquired and genetic forms of hemophilia
Genetic hemophilia is an
X-linked recessive disorder.
We want to monitor the patient's
clotting times with lab work.
You also want to monitor for complications
including internal and external bleeding.
Bleeding can go into the joints and
this can cause permanent joint destruction.
The pateint can have bleeding into
the brain and this can be life-threatening.
Management includes the
patients receiving clotting factors.
Thank you for watching
this lecture on hemophilia.