00:01 We’ll go onto a topic called choledochal cyst. 00:04 When you hear choledochal, it means that now you’re in your biliary tree. 00:09 Not cholecystitis, you’re not thinking about the gallbladder, but this is literally in the biliary tree. 00:15 A choledochal cyst is not a stone, by the way. 00:19 So this is not a choledocolithiasis. This is a choledochal cyst, a congenital issue in which there is dilation of the biliary tree. 00:27 Your child is going to present with the abdominal pain. 00:30 There is going to be jaundice, and unfortunately, with this cyst, there might be pancreatitis taking place. 00:36 With the choledochal cyst in a child congenitally -- wow, you’re worried about malignancy. 00:42 Surgery is your next step of management. Do not mess around. 00:48 Under choledochal cyst, there’s something called Caroli syndrome, autosomal recessive condition. It’s a saccular dilation of the intra-hepatic bile duct. Whereas, when we talked about choledochal cyst, it could be intra or extra-hepatic. If it’s intra-hepatic, you call this Caroli syndrome. 01:06 Chronic cholangitis may cause cirrhosis and require transplantation. 01:10 Remember, this is genetic, and anytime that there is stasis of your bile, now, what are you worried about? Infection. It’s called cholangitis. 01:19 And in a young patient, my goodness, that liver is so tender. 01:23 There’s every possibility that the child’s liver might go rapidly into cirrhosis, and your only step of management here is liver transplantation.
The lecture Choledochal Cysts by Carlo Raj, MD is from the course Pancreatic and Biliary Tract Diseases: Basic Principles with Carlo Raj.
Which of the following conditions has a high risk for malignant transformation?
A patient is diagnosed with a choledochal cyst and wants to know how the condition developed. How would you explain the condition to the patient?
Which of the following describes Caroli’s syndrome?
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